| Table 1: Transmissible spongiform encephalopathies
|
| Syndrome (year of first report) | Features |
| Human | |
| Creutzfeldt-Jakob disease (1920)2 | Dementia; myoclonus; changes on electroencephalogram
|
| Gerstmann-Straussler-Scheinker syndrome (1928)2 | Dementia; ataxia; exclusively familial
|
| Kuru (1957)3 | Ataxia; tremor; associated with mourning rites among the Fore people of New Guinea
|
| Fatal familial insomnia (1986)4 | Insomnia; ataxia; myoclonus
|
| Variant Creutzfeldt-Jakob disease (1996)1 | Low age at onset; ataxia; unique neuropathology
|
| Animal | |
| Scrapie (sheep and goats) (c. 1750)5 | Ataxia; pruritus
|
| Transmissible mink encephalopathy (1947)5 | Ataxia; somnolence
|
| Chronic wasting disease of elk (1980)5 | Behavioural changes; wasting
|
| Bovine spongiform encephalopathy (1987)6 | Ataxia; wasting
|
| Spongiform encephalopathy of exotic ungulates (1988)7
| Ataxia; wasting |
| Feline spongiform encephalopathy (1990)8 | Ataxia; behavioural changes
|