Creutzfeldt-Jakob Disease

CJD-Surveillance System

Statistics

• Referrals of Suspected CJD Reported to CJD-SS
• CJD Cases Reported to CJD-SS
• CJD Cases Reported by Province
• Incidence of CJD Cases Reported to CJD-SS in Canada

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Referrals of Suspected CJD Reported by CJD-SS¹,
1997-2008² as of February 28, 2009

Year of Reporting	Number of Referrals
1997	4
1998	43
1999	63
2000	82
2001	101
2002	103
2003	75
2004	90
2005	96
2006	78
2007	101
2008	99
2009	11
Total Referrals	946

Notes:
¹CJD-SS began in April 1998
²Data before April 1998 are retrospective and partial, data from 1999 to 2006 are complete, and data for 2007 and 2008 are provisional

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CJD Deaths Reported by CJD-SS¹, 1994-2008² as of February 28, 2009

Deaths of Definite and Probable CJD
Year	Sporadic	Iatrogenic	Familial	GSS	FFI	vCJD	Total
1994	2	0	0	0	0	0	2
1995	3	0	0	0	0	0	3
1996	13	0	0	0	0	0	13
1997	16	0	1	1	0	0	18
1998	22	1	0	1	0	0	24
1999	26	2	2	1	0	0	31
2000	32	0	0	3	0	0	35
2001	27	0	2	1	0	0	30
2002	31	0	2	2	0	1	36
2003	27	1	1	0	0	0	29
2004	42	0	1	0	0	0	43
2005	40	0	0	2	0	0	42
2006	37	0	1	3	1	0	42
2007	27	0	0	2	0	0	29
2008	13	0	0	0	0	0	13
2009	0	0	0	0	0	0	0
Total	358	4	10	16	1	1	390

Notes:
¹CJD-SS began in April 1998
²Data before April 1998 are retrospective and partial, data from 1999 to 2007 are complete, and data for 2008 and 2009 are provisional
*This number contains 4 cases that were preliminarily classified on limited data

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CJD Cases by Province/Territory As of February 28, 2009

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Incidence of CJD¹ Deaths Reported by CJD-SS in Canada As of February 28, 2009

Year of Death	Total CJD Cases	Population of Canada	Incidence Rate
1999	31	30,403,878	1.02
2000	35	30,689,035	1.14
2001	30	31,021,251	0.97
2002¹	36	31,372,587	1.15
2003	29	31,669,150	0.92
2004	43	32,069,999	1.34
2005	42	32,378,122	1.30
2006	42	32,730,213	1.28
2007	29	33,091,228	0.88
2008²	13	33,223,840	0.39
2009²			0.00

World Wide average occurrence of CJD is approximately 1-2 per million population

Notes:
¹ As of September 2002, CJD cases include both definite and probable cases of CJD
²Data from 1999 to 2007 are complete, and data for 2008 and 2009 are provisional
2008 Population Source: http://www.statcan.ca/Daily/English/080625/d080625b.htm

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National Microbiology Laboratory Genetics and Prion Disease program (HGPD)