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Creutzfeldt-Jakob Disease

CJD-Surveillance System

Statistics

 

Data tables are also available in an alternate format for downloading or viewing:
PDF Version Statistics March 2011 PDF Version (68 KB - 4 pages)

Referrals of Suspected CJD Reported by CJDSS1,
1997-20112 as of March 31, 2011
1 CJDSS began in April 1998
2 Data before April 1998 are retrospective and partial, data from 1999 to 2009 are complete, and data for 2010 - 2011 are provisional
Year of Reporting Number of Referrals
1997 4
1998 43
1999 63
2000 82
2001 101
2002 103
2003 75
2004 90
2005 97
2006 78
2007 101
2008 100
2009 104
2010 75
2011 23
Total Referrals 1139

CJD Deaths Reported by CJDSS1, 1994-20112 as of March 31, 2011
1 CJDSS began in April 1998
2 Data before April 1998 are retrospective and partial, data from 1999 to 2009 are complete, and data for 2009 - 2011 are provisional
3 Final classification of 49 cases from 2009, 2010, 2011 is pending.
Deaths of Definite and Probable CJD
Year Sporadic Iatrogenic Familial GSS FFI vCJD Total
1994 2 0 0 1 0 0 3
1995 3 0 0 0 0 0 3
1996 13 0 0 0 0 0 13
1997 16 0 1 1 0 0 18
1998 22 1 0 1 0 0 24
1999 26 2 2 1 0 0 31
2000 32 0 0 3 0 0 35
2001 27 0 2 1 0 0 30
2002 31 0 2 2 0 1 36
2003 27 1 1 0 0 0 29
2004 42 0 1 0 0 0 43
2005 42 0 0 2 0 0 44
2006 39 0 1 3 1 0 44
2007 34 0 0 4 0 0 38
2008 46 0 1 0 0 0 47
2009 47 0 3 2 0 0 52
2010 26 0 1 0 0 0 27
2011 0 0 0 0 0 0 0
Total 475 4 15 21 1 1 517

CJD Cases by Province/Territory as of March 31, 2011

CJD Cases by Province/Territory

Incidence of CJD Deaths Reported by CJDSS in Canada as of March 31, 2011

NOTES:
1 As of September 2002, CJD cases include both definite and probable cases of CJD
2 Data from 1999 to 2009 are complete, and data for 2010 and 2011 are provisional
2010 Population Source: Statistics Canada, Demography Division
Final classification of 49 cases from 2009, 2010, 2011 is pending

Year of Death Total CJD Cases Population of Canada Incidence Rate
1999 31 30,401,286 1.02
2000 35 30,685,730 1.14
2001 30 31,019,020 0.97
2002¹ 36 31,353,656 1.15
2003 29 31,639,670 0.92
2004 43 31,940,676 1.35
2005 44 32,245,209 1.36
2006 44 32,576,074 1.35
2007 38 32,931,956 1.15
2008 47 33,327,337 1.41
2009 52 33,739,814 1.54
2010² 27 33,841,500 0.80
2011² 0 34,019,075 0.00

World Wide average occurrence of CJD is approximately 1-2 per million population

This link will take you to another Web site (external site) European Creutzfeldt Jakob Disease Surveillance Network


National Microbiology Laboratory Genetics and Prion Disease program (HGPD)